From: The outcome of genetic and non-genetic pediatric cardiomyopathies
Diagnosis CMP Type | ||||||
---|---|---|---|---|---|---|
DCM | HCM | RCM | LVNC | Total | ||
Gender | Male | 80 | 32 | 1 | 4 | 117 |
Female | 80 | 28 | 3 | 1 | 112 | |
Mode of presentation | Heart failure | 118 | 47 | 4 | 1 | 170 |
Cardiogenic shock | 29 | 1 | 0 | 0 | 30 | |
Asymptomatic | 13 | 12 | 0 | 4 | 29 | |
Syndromic | Yes | 14 | 3 | 0 | 1 | 18 |
No | 146 | 57 | 4 | 4 | 211 | |
Primary or secondary CMP | Primary | 76 | 27 | 4 | 3 | 110 |
Secondary | 84 | 33 | 0 | 2 | 119 | |
Suspected viral illness | Yes | 18 | 0 | 0 | 0 | 18 |
No | 113 | 60 | 4 | 5 | 182 | |
Unknown | 29 | 0 | 0 | 0 | 29 | |
Genetic study | Positive/Abnormal | 21 | 27 | 0 | 2 | 50 |
Negative/Normal | 39 | 0 | 0 | 0 | 39 | |
Unknown | 100 | 33 | 4 | 3 | 140 | |
Admission on first presentation | Yes | 112 | 34 | 3 | 0 | 149 |
No | 31 | 26 | 1 | 5 | 63 | |
Unknown | 17 | 0 | 0 | 0 | 17 | |
Consanguineous parents | Yes | 41 | 22 | 0 | 1 | 64 |
No | 18 | 1 | 0 | 0 | 19 | |
Unknown | 101 | 37 | 4 | 4 | 146 | |
Family history of CMP | Yes | 17 | 0 | 0 | 0 | |
No | 106 | 1 | 0 | 0 | ||
Unknown | 12 | 0 | 0 | 0 | ||
Final results | Static | 17 | 15 | 3 | 5 | 40 |
Normalized | 57 | 0 | 0 | 0 | 57 | |
Improving | 29 | 6 | 0 | 0 | 35 | |
Expired | 48 | 39 | 1 | 0 | 88 | |
Lost | 9 | 0 | 0 | 0 | 9 | |
Alive dead | Alive | 103 | 21 | 3 | 5 | 132 |
Expired | 48 | 39 | 1 | 0 | 88 | |
Lost | 9 | 0 | 0 | 0 | 9 |